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Case 21.1 – Oesophageal Carcinoma

Category: Medicine | Discipline: Gastroenterology | Setting: Outpatient Clinic

Case

Mr. David Thompson, a 68-year-old retired builder, presents to the gastroenterology outpatient clinic with a 3-month history of progressive dysphagia. He describes initial difficulty swallowing solid foods, which has now progressed to include soft foods and liquids. He has lost 8 kg during this period and reports a feeling of food "sticking" in his chest. He has a 45-pack-year smoking history and drinks 2-3 standard drinks daily. He has also noticed regurgitation of undigested food and occasional chest discomfort unrelated to exertion.

Vital signs: BP 135/80 mmHg, HR 78 bpm, RR 16/min, Temp 36.8°C, SpO2 98% on room air. BMI 21 (previously 24 three months ago)

Questions

1. What are the key red flag features in Mr. Thompson's presentation that warrant urgent investigation?

Red flag features present in this case include:

  • Progressive dysphagia: Starting with solids and progressing to liquids suggests mechanical obstruction
  • Significant unintentional weight loss: Loss of 8kg over 3 months is substantial and concerning for malignancy
  • Age >55 years: Increased risk of upper GI malignancy
  • Smoking history: Major risk factor for oesophageal carcinoma, particularly squamous cell carcinoma
  • Alcohol consumption: Synergistic effect with smoking in increasing cancer risk

The combination of progressive dysphagia with weight loss in a patient with significant risk factors requires urgent investigation, typically with upper GI endoscopy within 2 weeks (urgent cancer pathway).

2. What are the two main histological types of oesophageal carcinoma, and how do their epidemiology and risk factors differ?

Squamous Cell Carcinoma (SCC):

  • Historically the most common type worldwide, though incidence is decreasing in Western countries
  • Typically occurs in the upper and middle third of the oesophagus
  • Major risk factors: smoking, alcohol, achalasia, caustic injury, Plummer-Vinson syndrome
  • More common in lower socioeconomic groups
  • Higher incidence in certain geographical areas (e.g., parts of Asia, Iran, South Africa)

Adenocarcinoma:

  • Rapidly increasing incidence in Western countries, now the most common type in developed nations
  • Typically arises in the lower third of the oesophagus
  • Major risk factors: Barrett's oesophagus (the main precursor), chronic gastro-oesophageal reflux disease (GORD), obesity, smoking
  • More common in Caucasian males
  • Associated with metabolic syndrome

Mr. Thompson's smoking and alcohol history places him at risk for both types, though his symptoms and risk factors are compatible with either histology.

3. What is Barrett's oesophagus and why is it clinically significant?

Barrett's oesophagus is a condition where the normal stratified squamous epithelium of the lower oesophagus is replaced by metaplastic columnar epithelium, typically containing goblet cells (intestinal metaplasia).

Pathophysiology:

  • Develops as a response to chronic acid exposure from GORD
  • The columnar epithelium is more resistant to acid than squamous epithelium
  • Represents an adaptive but pre-malignant change

Clinical Significance:

  • Main precursor lesion for oesophageal adenocarcinoma
  • Risk of malignant transformation approximately 0.2-0.5% per year
  • Dysplasia in Barrett's significantly increases cancer risk:
    • Low-grade dysplasia: 0.5-1% annual cancer risk
    • High-grade dysplasia: 7-10% annual cancer risk
  • Requires surveillance endoscopy with systematic biopsies
  • Surveillance intervals depend on length of Barrett's segment and presence of dysplasia

Management:

  • PPI therapy to control acid reflux
  • Regular surveillance endoscopy (intervals based on dysplasia grade and segment length)
  • Endoscopic intervention (ablation or resection) for dysplasia
  • Lifestyle modifications: weight loss, smoking cessation, alcohol reduction
4. What investigations would you arrange for Mr. Thompson and in what order of priority?

Urgent investigations:

  • Upper GI endoscopy (OGD) with biopsy: Gold standard for diagnosis
    • Direct visualization of the tumour
    • Biopsy for histological confirmation
    • Assessment of location, size, and extent
    • Should be performed within 2 weeks (urgent suspected cancer pathway)

Staging investigations (if cancer confirmed):

  • CT chest, abdomen, and pelvis with contrast: To assess for:
    • Local invasion
    • Regional lymphadenopathy
    • Distant metastases (liver, lungs, peritoneum)
  • PET-CT scan: Increasingly used for:
    • Detection of distant metastases
    • Assessment of nodal involvement
    • Evaluation of treatment response
  • Endoscopic ultrasound (EUS): Most accurate for:
    • Depth of tumour invasion (T staging)
    • Local lymph node assessment (N staging)
    • May allow FNA of suspicious nodes
  • Laparoscopy: May be considered in gastro-oesophageal junction tumours to exclude peritoneal disease

Other investigations:

  • Full blood count (anaemia from chronic blood loss)
  • Renal and liver function tests
  • Nutritional assessment
  • Pulmonary function tests (if surgery being considered)
  • Cardiology assessment if significant cardiac history
5. Outline the TNM staging system for oesophageal cancer and explain its clinical relevance.

The TNM (Tumour, Node, Metastasis) staging system is used to classify the extent of oesophageal cancer:

T (Primary Tumour):

  • Tis: High-grade dysplasia/carcinoma in situ
  • T1a: Invades lamina propria or muscularis mucosae
  • T1b: Invades submucosa
  • T2: Invades muscularis propria
  • T3: Invades adventitia
  • T4a: Invades adjacent structures (pleura, pericardium, diaphragm)
  • T4b: Invades unresectable structures (aorta, vertebral body, trachea)

N (Regional Lymph Nodes):

  • N0: No regional lymph node metastases
  • N1: 1-2 regional lymph nodes involved
  • N2: 3-6 regional lymph nodes involved
  • N3: ≥7 regional lymph nodes involved

M (Distant Metastasis):

  • M0: No distant metastases
  • M1: Distant metastases present

Clinical Relevance:

  • Treatment planning: Stage determines treatment approach:
    • Early stage (T1a N0): May be suitable for endoscopic resection
    • Locally advanced (T2-3, N0-1): Neoadjuvant chemotherapy/chemoradiotherapy followed by surgery
    • Advanced disease (T4b or M1): Palliative treatment
  • Prognosis: Stage is the most important prognostic factor
    • Stage I: 5-year survival ~80%
    • Stage II: 5-year survival ~30-40%
    • Stage III: 5-year survival ~10-20%
    • Stage IV: 5-year survival \<5%
  • MDT discussion: Staging information is essential for multidisciplinary team decision-making
6. What are the treatment options for oesophageal carcinoma, and how is the treatment approach determined?

Treatment is determined by stage, patient fitness, and tumour histology, discussed in a multidisciplinary team (MDT) meeting.

Curative Treatment Options:

1. Endoscopic Therapy (Early disease - T1a):

  • Endoscopic mucosal resection (EMR)
  • Endoscopic submucosal dissection (ESD)
  • Radiofrequency ablation (for Barrett's with dysplasia)
  • Suitable for superficial lesions without lymph node involvement

2. Surgery:

  • Oesophagectomy: Main curative surgical option
    • Ivor-Lewis (right thoracotomy + laparotomy)
    • Three-stage/McKeown (right thoracotomy + laparotomy + neck anastomosis)
    • Transhiatal approach
    • Minimally invasive oesophagectomy increasingly used
  • Significant morbidity and mortality (perioperative mortality ~3-5%)
  • Requires adequate cardiopulmonary reserve

3. Neoadjuvant Therapy:

  • Neoadjuvant chemotherapy: Used for adenocarcinoma (typically ECF or FLOT regimen)
  • Neoadjuvant chemoradiotherapy: May be used for squamous cell carcinoma
  • Improves survival compared to surgery alone
  • Allows downstaging of tumour
  • Given for locally advanced resectable disease (typically T2-3, N0-1)

4. Definitive Chemoradiotherapy:

  • For patients unfit for surgery
  • Particularly for squamous cell carcinoma
  • May achieve cure in selected cases

Palliative Treatment Options:

  • Palliative chemotherapy: For metastatic disease in fit patients
  • Palliative radiotherapy: For bleeding, pain, or obstruction
  • Oesophageal stenting: For dysphagia relief
  • Nutritional support:
    • Dietary modification
    • Enteral feeding (nasogastric, nasojejunal, or gastrostomy)
    • Parenteral nutrition if required
  • Best supportive care: Including pain management and psychological support

Treatment Decision Factors:

  • Tumour stage (most important)
  • Patient performance status and comorbidities
  • Nutritional status
  • Patient preference
  • Tumour location and histology
7. Mr. Thompson is diagnosed with T3N1M0 adenocarcinoma of the lower oesophagus. What specific nutritional concerns would you address, and what supportive measures might be needed during his treatment?

Nutritional Concerns:

  • Pre-existing malnutrition: Already lost 8kg (significant weight loss)
  • Progressive dysphagia: Limiting oral intake
  • Cancer cachexia: Increased metabolic demands
  • Treatment-related factors:
    • Neoadjuvant chemotherapy: nausea, mucositis, anorexia
    • Surgery: prolonged recovery, altered GI anatomy
    • Radiation: oesophagitis, odynophagia

Nutritional Assessment:

  • Detailed dietary history and nutritional screening (e.g., MUST score)
  • Biochemical markers: albumin, prealbumin (though affected by inflammatory response)
  • Body composition assessment
  • Swallowing assessment

Nutritional Support Strategies:

Pre-treatment optimization:

  • Dietitian review and individualized nutritional plan
  • High-calorie, high-protein diet modifications:
    • Small, frequent meals
    • Soft, moist foods
    • Food fortification
  • Oral nutritional supplements
  • Consider early enteral feeding if inadequate oral intake:
    • Nasogastric or nasojejunal feeding
    • Radiologically inserted gastrostomy (RIG) or jejunostomy if prolonged support anticipated

During treatment:

  • Continue nutritional support
  • Manage treatment side effects affecting nutrition
  • Regular weight and nutritional status monitoring
  • Feeding jejunostomy often placed at time of oesophagectomy for post-operative nutrition

Other Supportive Measures:

  • Smoking cessation: Critical for surgical outcomes and overall prognosis
  • Alcohol reduction: Cessation support if needed
  • Psychological support: Diagnosis of cancer and major surgery
    • Clinical psychology/psychiatry referral
    • Support groups
    • Information provision
  • Symptom management:
    • Dysphagia management strategies
    • Pain control
    • Anti-emetics for chemotherapy
    • PPI therapy for reflux symptoms
  • Prehabilitation program:
    • Exercise program to improve fitness
    • Respiratory physiotherapy
    • Optimisation of comorbidities
  • Dental assessment: Prior to radiotherapy
  • Clinical nurse specialist support: Coordination of care and patient support

A multidisciplinary approach involving surgeons, oncologists, dietitians, specialist nurses, physiotherapists, and other allied health professionals is essential for optimal outcomes.